Nakazato Y, Shimazu K, Tamura N, Hamaguchi K
Department of Neurology, Saitama Medical School.
Rinsho Shinkeigaku. 1996 Aug;36(8):940-3.
We described two cases of idiopathic segmental anhidrosis. Case 1 was a 47-year-old man, who noticed anhidrosis on the right side of face and chest during body heating. Case 2 was a 54-year-old woman, who complained of anhidrosis on the left side of face and upper chest during exercise. Both cases had neither somatic neurological deficit nor autonomic failure except for anhidrosis pupil size and deep tendon reflexes were normal. Reflex sweating to pilocarpine was exaggerated in the anhidrotic areas in both cases, suggesting lesions in the preganglionic sudomotor nerves. Abnormal laboratory finding was elevated serum rheumatoid factor level in only case 2. Segmental anhidrosis was static for 1.5 year and one year, respectively. The previous literature contains similar four cases. Idiopathic segmental anhidrosis may be an abortive form of Ross' syndrome (tonic pupil, hyporeflexia and segmental anhidrosis).
我们描述了两例特发性节段性无汗症。病例1是一名47岁男性，在身体受热时发现面部右侧和胸部无汗。病例2是一名54岁女性，她主诉运动时面部左侧和上胸部无汗。两例患者除无汗外均无躯体神经功能缺损和自主神经功能衰竭，瞳孔大小和腱反射正常。两例患者在无汗区域对毛果芸香碱的反射性出汗均增强，提示节前泌汗神经存在病变。仅病例2的实验室检查异常为血清类风湿因子水平升高。节段性无汗症分别持续了1.5年和1年。既往文献中有类似的4例病例。特发性节段性无汗症可能是罗斯综合征（强直性瞳孔、反射减退和节段性无汗症）的一种顿挫型。
