部分未闭冠状静脉窦综合征合并永存左上腔静脉、右上腔静脉缺如及右侧心包缺损。

Partially unroofed coronary sinus syndrome with persistent left superior vena cava, absent right superior vena cava and right-sided pericardial defect.

作者信息

Yilmaz A T, Arslan M, Demirkiliç U, Kuralay E, Ozal E, Tatar H, Oztürk O Y

机构信息

Department of Cardiovascular Surgery, Gülhane Military Medical Academy, Ankara, Turkey.

出版信息

Eur J Cardiothorac Surg. 1996;10(11):1027-9. doi: 10.1016/s1010-7940(96)80410-6.

DOI:10.1016/s1010-7940(96)80410-6

PMID:8971519

Abstract

Partially unroofed coronary sinus syndrome with persistent left superior vena cava is a rare congenital anomaly. It frequently produces a right-to-left shunt. We report a case in which a large left-to-right shunt was present, because of the obstruction to left ventricular inflow as a result of the dilated coronary sinus. This abnormality was associated with absent right superior vena cava and a partial pericardial defect on the right side.

摘要

部分未被覆冠状静脉窦综合征合并永存左上腔静脉是一种罕见的先天性异常。它常导致右向左分流。我们报告一例因扩张的冠状静脉窦导致左心室流入道梗阻而出现大量左向右分流的病例。这种异常与右上腔静脉缺如及右侧部分心包缺损有关。