Warren R H, Alderson S H
Pulmonary Medicine Section, UAMS, USA.
J Ark Med Soc. 1996 Dec;93(7):333-7.
The Pulmonary Medicine Section of the Department of Pediatrics of the University of Arkansas for Medical Sciences has recently developed an association with the Muscular Dystrophy Association Clinic held at Arkansas Children's Hospital. The slowly progressive, insidious onset of pulmonary problems associated with Duchenne-type muscular dystrophies and other degenerative muscle disorders indicated a need for a aggressive monitoring and treatment plan for these children and their caregivers. We have developed a Respiratory Care Handbook for families with information on the pulmonary consequences of these diseases including pathophysiology, pulmonary function tests, respiratory treatments including mechanical ventilatory support, and anticipation and prevention of pulmonary crises. In addition, we have introduced for the physician a formal monitoring and treatment regimen driven by changes in the vital capacity lung volume. The substance of this plan is presented in this manuscript.
阿肯色大学医学科学学院儿科学系的肺病科最近与阿肯色儿童医院举办的肌肉萎缩症协会诊所建立了合作关系。与杜氏型肌营养不良症和其他退行性肌肉疾病相关的肺部问题起病缓慢、隐匿，这表明需要为这些儿童及其护理人员制定积极的监测和治疗计划。我们为家庭编写了一本呼吸护理手册，其中包含有关这些疾病的肺部后果的信息，包括病理生理学、肺功能测试、呼吸治疗（包括机械通气支持）以及肺部危机的预测和预防。此外，我们为医生引入了一种由肺活量肺容积变化驱动的正式监测和治疗方案。本方案的内容将在本手稿中呈现。
