穆兰线性皮肤萎缩症：用泛硫乙胺治疗。

Linear atrophoderma of Moulin: treatment with Potaba.

作者信息

Artola Igarza J L, Sánchez Conejo-Mir J, Corbí Llopis M R, Linares Barrios M, Casals Andreu M, Navarrete Ortega M

机构信息

Department of Dermatology, Virgen del Rocío University Hospital, School of Medicine, Seville, Spain.

出版信息

Dermatology. 1996;193(4):345-7. doi: 10.1159/000246288.

DOI:10.1159/000246288

PMID:8993965

Abstract

Linear atrophoderma is a rare disease, first described by Moulin in 1992 in 5 patients, clinically characterized by hyperpigmented, depressed band-like areas along Blaschko's lines. To date, the disease has no effective treatment. We report the seventh case of this condition in a 16-year-old girl and discuss clinical and histopathologic findings, emphasizing the benefit of the potassium aminobenzoate (Potaba) treatment which provided an early stabilization of the skin lesions.

摘要

线状皮肤萎缩症是一种罕见疾病，1992年由穆兰首次描述，涉及5例患者，临床特征为沿布拉斯科线出现色素沉着、凹陷的带状区域。迄今为止，该疾病尚无有效治疗方法。我们报告了一名16岁女孩患此病的第七个病例，并讨论了临床和组织病理学发现，强调了对氨基苯甲酸钾（Potaba）治疗的益处，该治疗使皮肤病变得以早期稳定。