Hazan E, Baillot F, Rey C, Dupuis C
Am J Cardiol. 1977 Sep;40(3):463-6. doi: 10.1016/0002-9149(77)90173-4.
Isolated ventricular discordance is a very rare malformation, most often lethal in the first months of life. A patient with this lesion survived to age 9 years in spite of the coexistence of a complete form of atrioventricular (A-V) canal. Surgical repair with a Mustard procedure was associated with correction of the endocardial cushion defect. Situs inversus itself caused no problem. Although permanent complete A-V block occurred, the result has been satisfactory so far. This case is thought to be the first successful correction of this malformation.
孤立性心室不协调是一种非常罕见的畸形，通常在出生后的头几个月内致命。尽管存在完全型房室通道，但一名患有这种病变的患者存活至9岁。采用Mustard手术进行手术修复与心内膜垫缺损的矫正相关。内脏反位本身并未造成问题。虽然发生了永久性完全性房室传导阻滞，但迄今为止结果令人满意。该病例被认为是首例成功矫正这种畸形的病例。
