Zelop C, Benacerraf B
Department of Obstetrics and Gynecology, Brigham & Women's Hospital, Boston, Massachusetts, USA.
Ultrasound Obstet Gynecol. 1996 Dec;8(6):391-6. doi: 10.1046/j.1469-0705.1997.08060391.x.
The aim of this study was to determine the etiology, associated anomalies and outcome of fetuses with postural deformities and contractures of the upper extremities detected sonographically. Fifty-four fetuses with sonographically detected postural anomalies of the upper extremities were identified from our database. Sonographic findings and associated anomalies were tabulated on the basis of the original sonogram. Perinatal follow-up and/or karyotype were available in 52 cases from a review of the maternal and newborn medical records and pathology reports. Of the 52 fetuses with sonographically detected anomalies of the upper extremities, 44 (85%) were non-survivors and eight (15%) were survivors. Forty-three fetuses had associated sonographic abnormalities. Karyotyping performed in 44 cases revealed 26 cases (59%) of aneuploidy, with trisomy 18 accounting for 23/26 (88%). In the setting of a normal karyotype, a variety of genetic disorders were found, including syndromes involving the fetal dyskinesia/akinesia sequence. Disturbances in amniotic fluid occurred in 48% of the cases (24 fetuses with polyhydramnios and one with oligohydramnios). In conclusion, the sonographic detection of postural abnormalities of the upper extremities carries a guarded prognosis, with survival in 15% of fetuses and a high incidence of chromosomal defects.
本研究的目的是确定经超声检查发现的上肢姿势畸形和挛缩胎儿的病因、相关异常及结局。从我们的数据库中识别出54例经超声检查发现上肢姿势异常的胎儿。根据原始超声图像将超声检查结果和相关异常情况制成表格。通过查阅孕产妇和新生儿病历及病理报告,52例病例有围产期随访资料和/或核型分析结果。在这52例经超声检查发现上肢异常的胎儿中,44例(85%)为非存活者,8例(15%)为存活者。43例胎儿有相关的超声异常表现。44例进行了核型分析,其中26例(59%)为非整倍体,18三体占23/26(88%)。在核型正常的情况下,发现了多种遗传疾病,包括涉及胎儿运动障碍/运动不能序列的综合征。48%的病例(24例羊水过多和1例羊水过少)出现羊水异常。总之,超声检查发现上肢姿势异常预后不佳,仅15%的胎儿存活,且染色体缺陷发生率高。