Sarioğlu A, Tanyel F C, Büyükpamukçu N, Hiçsönmez A
Department of Pediatric Surgery, Faculty of Medicine, Hacettepe University, Ankara, Turkey.
J Pediatr Surg. 1997 Jan;32(1):117-8. doi: 10.1016/s0022-3468(97)90113-5.
Although rare, patients with Hirschsprung's disease (HD) may be admitted with colonic volvulus. Among 302 patients with HD two patients were admitted with colonic volvulus (0.66%). Involved segments were cecum and sigmoid colon. During the same period, 11 patients including those with HD were diagnosed with colonic volvulus. An aganglionic segment below sigmoid colon, and a freely mobile mesosigmoid seem to be the cause of sigmoid volvulus. However, extension of aganglionosis above the sigmoid colon in addition to anatomic tendency seems to result in volvulus of proximal segments. Because HD has been associated with colonic volvulus, children who present with colonic volvulus should be suspect for underlying HD.
虽然罕见，但患有先天性巨结肠症（HD）的患者可能因结肠扭转而入院。在302例HD患者中，有2例因结肠扭转入院（0.66%）。受累节段为盲肠和乙状结肠。在同一时期，包括HD患者在内的11例患者被诊断为结肠扭转。乙状结肠以下的无神经节段以及活动自如的乙状结肠系膜似乎是乙状结肠扭转的原因。然而，除了解剖学倾向外，乙状结肠以上无神经节症的扩展似乎导致了近端节段的扭转。由于HD与结肠扭转有关，出现结肠扭转的儿童应怀疑有潜在的HD。
