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[主动脉-左心室通道合并肺动脉瓣狭窄]

[Aortico-left ventricular tunnel associated with pulmonary valve stenosis].

作者信息

Martín Jiménez J, González Diéguez C C, Quero Jiménez C, Rico Gómez F, Bermúdez Cañete R, Quero Jiménez M

机构信息

Servicio de Cardiología Pediátrica, Hospital Ramón y Cajal, Madrid.

出版信息

Rev Esp Cardiol. 1996 Dec;49(12):921-4.

PMID:9026844
Abstract

Aortico-left ventricular tunnel is an unusual cardiac anomaly. The main clinical feature is early, severe aortic regurgitation, and surgical management is mandatory. Exceptionally this defect is associated with pulmonary valve stenosis. A case of a newborn with aortico-left ventricular tunnel plus pulmonary valve stenosis is reported. Initially she underwent percutaneous pulmonary valvuloplasty during diagnostic cardiac catheterization and with surgical closure of the tunnel later.

摘要

主动脉-左心室隧道是一种罕见的心脏异常。主要临床特征是早期严重主动脉瓣反流,手术治疗是必要的。极少数情况下,这种缺陷与肺动脉瓣狭窄相关。本文报道了一例患有主动脉-左心室隧道合并肺动脉瓣狭窄的新生儿病例。最初,她在诊断性心导管检查期间接受了经皮肺动脉瓣成形术,随后进行了隧道的手术闭合。

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