Mikus P M, Arpesella G, Hazan E, Neveux J Y
G Ital Cardiol. 1977;7(7):713-9.
The association between ventricular septal defect and pulmonary valve atresia is a rare congenital disease, which can provoke the compression of bronchioles, that make a high mortality rate possible in the first years of life. If this syndrome is tolerated, using a convenient medical therapy, it is possible to wait for a more suitable age for a complete correction, which must provide, besides V.S.D. closing, pulmonary valvular substitution by porcine aortic heterograft. The authors also report on their own experience of five cases surgically treated and studied from a pre- and postoperative hemodinamic point of view.
室间隔缺损与肺动脉瓣闭锁之间的关联是一种罕见的先天性疾病，它可引发细支气管受压，这使得在生命的头几年死亡率可能很高。如果通过适当的药物治疗耐受这种综合征，就有可能等待更合适的年龄进行完全矫正，除了关闭室间隔缺损外，还必须通过猪主动脉异种移植物进行肺动脉瓣置换。作者还报告了他们自己从术前和术后血液动力学角度对5例手术治疗和研究的经验。
