Bilbao J I, Pueyo J C, Longo J M, Arias M, Herrero J I, Benito A, Barettino M D, Perotti J P, Pardo F
Department of Radiology, Clínica Universitaria, Facultad de Medicina, Universidad de Navarra, Avenida Pio XII no. 36, E-31008 Pamplona, Spain.
Cardiovasc Intervent Radiol. 1997 Mar-Apr;20(2):112-9. doi: 10.1007/s002709900117.
To analyze the results obtained with percutaneous therapeutic procedures in patients with Budd-Chiari syndrome (BCHS).
Between August 1991 and April 1993, seven patients with BCHS were treated in our hospital. Three presented with a congenital web; in another three cases the hepatic veins and/or the inferior vena cava (IVC) were compromised after major hepatic surgery; one patient presented with a severe stenosis of the intrahepatic IVC due to hepatomegaly.
One of the patients with congenital web has required several new dilatations due to restenosis; one patient required a transjugular intrahepatic portosystemic shunt procedure while awaiting a liver transplantation. The two postsurgical patients with stenosed hepatic veins did not require any new procedure after the placement of metallic endoprostheses. However, the patient with liver transplantation presented IVC restenosis after balloon angioplasty that required the deployment of metallic endoprostheses. In the patient with hepatomegaly a self-expandable prosthesis was placed in the intrahepatic portion of the IVC before (4 months) a liver transplantation.
Interventional therapeutic techniques offer a wide variety of possibilities for the treatment of patients with BCHS. For IVC stenoses, the results obtained with balloon angioplasty are at least as good as those obtained with surgery.
分析布加综合征（BCHS）患者经皮治疗的结果。
1991年8月至1993年4月，我院对7例布加综合征患者进行了治疗。3例为先天性膜性狭窄；另外3例在肝脏大手术后肝静脉和/或下腔静脉（IVC）受损；1例因肝肿大导致肝内IVC严重狭窄。
1例先天性膜性狭窄患者因再狭窄需要多次扩张；1例患者在等待肝移植期间需要行经颈静脉肝内门体分流术。2例肝静脉狭窄的术后患者在植入金属内支架后无需任何新的治疗。然而，肝移植患者在球囊血管成形术后出现IVC再狭窄，需要植入金属内支架。对于肝肿大患者，在肝移植前（4个月）在肝内IVC段植入了自膨式支架。
介入治疗技术为布加综合征患者的治疗提供了多种可能性。对于IVC狭窄，球囊血管成形术的效果至少与手术相当。
