家族性痉挛性截瘫的电生理研究
Electrophysiological studies in familial spastic paraplegia.
作者信息
McLeod J G, Morgan J A, Reye C
出版信息
J Neurol Neurosurg Psychiatry. 1977 Jun;40(6):611-5. doi: 10.1136/jnnp.40.6.611.
Abstract
Motor and sensory conduction studies have been performed in 10 patients from three families with uncomplicated familial spastic paraplegia whose ages ranged from 4 to 41 years. In all cases the values fell within the control range. The findings may be contrasted with those in Friedreich's ataxia and some other spinocerebellar degenerations in which peripheral nerve abnormalities are present.
摘要
对来自三个家族的10例无并发症的家族性痉挛性截瘫患者进行了运动和感觉传导研究，这些患者年龄在4岁至41岁之间。所有病例的值均在正常对照范围内。这些发现可与弗里德赖希共济失调和其他一些存在周围神经异常的脊髓小脑变性的情况形成对比。
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