Milian Masanet A, Bagán Sebastián J V, Basterra Alegría J, Jimênez Soriano Y, Lloria de Miguel E
Medicina Bucal, Facultad de Medicina y Odontología de Valencia.
Acta Otorrinolaringol Esp. 1996 Nov-Dec;47(6):475-8.
Histiocytosis X is a group of disorders of the reticuloendothelial system that have different clinical features and common histological characteristics, including abnormal proliferation of Langerhans cells. Eosinophilic granuloma is a localized form of histiocytosis affecting one or more bones. A case report is made of a patient diagnosed as histiocytosis X whose first manifestation was the appearance of an orosinusal communication. The lesions were located in the maxillary bones and produced large osteolytic lesions. No other bones were affected. In spite of surgery and radiotherapy, the disease recurred at 12 months.
组织细胞增多症X是一组网状内皮系统疾病，具有不同的临床特征和共同的组织学特征，包括朗格汉斯细胞异常增殖。嗜酸性肉芽肿是组织细胞增多症的一种局限性形式，可累及一块或多块骨骼。本文报告一例诊断为组织细胞增多症X的患者，其首发表现为出现鼻窦交通。病变位于上颌骨，产生大片骨质溶解病变。未累及其他骨骼。尽管进行了手术和放疗，疾病仍在12个月后复发。
