对一名患有某种类型莱迪希细胞发育不全的表型女性进行腹腔镜双侧性腺切除术。

Laparoscopic bilateral gonadectomy in a phenotypic woman with a form of Leydig cell hypoplasia.

作者信息

Qasim S M, Sachdev R

机构信息

UMDNJ-Robert Wood Johnson Medical School, Department of Obstetrics, Gynecology, 303 George Street, Suite 250, New Brunswick, NJ 08901, USA.

出版信息

J Am Assoc Gynecol Laparosc. 1996 Feb;3(2):313-6. doi: 10.1016/s1074-3804(96)80021-1.

DOI:10.1016/s1074-3804(96)80021-1

PMID:9050648

Abstract

A 22-year-old phenotypic woman with an XY karyotype underwent laparoscopic gonadectomy after a comprehensive evaluation for primary amenorrhea. Pathology revealed primitive testicular support elements with absent Leydig cells bilaterally. This case illustrates the fact that, with a thorough preoperative workup, patients expressing various forms of male pseudohermaphroditism can now be treated appropriately by laparoscopy instead of laparotomy.

摘要

一名22岁核型为XY的表型女性，因原发性闭经接受全面评估后，进行了腹腔镜性腺切除术。病理显示双侧有原始睾丸支持组织，无Leydig细胞。该病例表明，通过全面的术前检查，现在可以通过腹腔镜而非剖腹手术对表现为各种形式男性假两性畸形的患者进行适当治疗。