Liang C D, Huang S C, Su W J
Department of Pediatrics, Chang Gung Memorial Hospital, Kaohsiung, Taiwan ROC.
J Formos Med Assoc. 1997 Feb;96(2):121-4.
Tetralogy of Fallot (TOF) and patent ductus arteriosus complicated by pulmonary vascular obstructive disease (PVOD) and hemoptysis in a 5-year-old girl are described. The echocardiogram was typical of TOF, as well as ductus arteriosus and right aortic arch. Cardiac catheterization revealed a pulmonary vascular resistance of 44 hybrid resistance units, and the pulmonary-to-systemic resistance ratio was 1.4. Diagnosis of PVOD was made by cardiac catheterization. Angiography revealed a bronchial artery arising from the left subclavian artery. PVOD itself, rupture of a bronchial artery or both, were considered the contributory causes of hemoptysis in this patient.
本文描述了一名5岁女孩，患有法洛四联症（TOF）和动脉导管未闭，并伴有肺血管阻塞性疾病（PVOD）及咯血。超声心动图显示为典型的法洛四联症，伴有动脉导管未闭和右位主动脉弓。心导管检查显示肺血管阻力为44混合阻力单位，肺循环与体循环阻力比值为1.4。通过心导管检查确诊为PVOD。血管造影显示一条支气管动脉发自左锁骨下动脉。PVOD本身、支气管动脉破裂或两者共同作用，被认为是该患者咯血的原因。
