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新生儿期出现的肛周室管膜瘤。

Perianal ependymoma presenting in the neonatal period.

作者信息

Webber E M, Fraser R B, Resch L, Giacomantonio M

机构信息

Department of Surgery, I.W.K.-Grace Health Centre, Dalhousie University, Halifax, Nova Scotia, Canada.

出版信息

Pediatr Pathol Lab Med. 1997 Mar-Apr;17(2):283-91.

PMID:9086535
Abstract

Extraspinal ependymomas are a rare type of glioma that may arise in the sacrococcygeal region, presenting as a pelvic mass in an infant or child. Ependymoma presenting in the newborn period has not been described previously. Herein we describe a case of a newborn boy who presented with a perianal ependymoma, which was subsequently found to have presacral extension. The major diagnostic challenge this case presented was to rule out the alternative diagnosis of sacrococcygeal teratoma or a developmental malformation/heterotopia.

摘要

脊柱外室管膜瘤是一种罕见的胶质瘤类型,可发生于骶尾区域,在婴儿或儿童中表现为盆腔肿块。此前尚未有关于新生儿期出现室管膜瘤的报道。在此,我们描述一例新生儿男婴,其患有肛周室管膜瘤,随后发现肿瘤已向骶前延伸。该病例面临的主要诊断挑战是排除骶尾畸胎瘤或发育畸形/异位的其他诊断。

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Pediatric Extraspinal Sacrococcygeal Ependymoma: Report of Two Cases and Literature Review.小儿脊柱外骶尾部室管膜瘤:2例报告及文献复习
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