心肌梗死与莱利-戴综合征的关联。

Myocardial infarction association with the Riley-Day syndrome.

作者信息

Reshef R, Aderka D, Suprun H, Manelis G, Manelis J

出版信息

Am Heart J. 1977 Oct;94(4):486-90. doi: 10.1016/s0002-8703(77)80044-6.

Abstract

The "sudden death" of a 23-year-old Ashkenazy Jew, suffering from "familial dysautonomia" was probably caused by an arrhythmia accompanying a myocardial infarction. Such a report is unique. Diffuse coronary atherosclerosis and direct myocardial "catecholamine cardiomyopathy" seem responsible for the myocardial damage. However, diversion of the endocardial blood flow toward dpicardium and a "coronary steal" phenomenon, both the result of a sudden catecholamine discharge, could aggravate the ischemic injury.

摘要

一名患有“家族性自主神经功能异常”的23岁阿什肯纳兹犹太人的“猝死”，可能是由心肌梗死伴发的心律失常所致。这样的报告很独特。弥漫性冠状动脉粥样硬化和直接的心肌“儿茶酚胺心肌病”似乎是心肌损伤的原因。然而，心内膜血流转向心外膜以及“冠状动脉窃血”现象，这两者都是儿茶酚胺突然释放的结果，可能会加重缺血性损伤。