Bosson N, Ducou le Pointe H, Boccon-Gibod L, Aït Bella S, Gruner M, Montagne J P
Service de Radiologie, Hôpital d'Enfants Armand-Trousseau, Paris.
J Radiol. 1997 Mar;78(3):227-9.
This case of mesenchymatous hamartoma in a nine-year-old boy, was an incidental finding on a chest X ray. CT and MRI suggested the diagnosis showing a large (9 x 11 x 14 cm) mass developed in the right lower lung with sharp margins, without any sign of pulmonary or mediastinal compression. This lesion contained fatty areas on both CT and MRI. It showed no calcification. It enhanced slightly after IV contrast. On T2 WI, it appeared lobulated with low signal intensity septa. Presence of fatty tissues and lobulated margins were suggestive of the diagnosis of mesenchymatous hamartoma. A 1.2 kg mass was surgically removed. The tumor was attached to the right lower lobe by a small pedicle. Pathological examination disclosed fatty and connective tissues. This rare observation shows a good correlation between CT, MR, surgery and pathological examination.
该例间叶性错构瘤发生于一名9岁男孩,是在胸部X线检查时偶然发现的。CT和MRI检查提示诊断,显示右肺下叶有一个大的(9×11×14cm)肿块,边界清晰,无任何肺或纵隔受压迹象。该病变在CT和MRI上均含有脂肪区域,无钙化表现,静脉注射造影剂后轻度强化。在T2加权像上,肿块呈分叶状,有低信号强度的分隔。脂肪组织的存在和分叶状边缘提示间叶性错构瘤的诊断。通过手术切除了一个1.2kg的肿块。肿瘤通过一个小蒂附着于右下叶。病理检查发现为脂肪组织和结缔组织。这一罕见病例显示了CT、MR、手术及病理检查之间具有良好的相关性。