Cory R C, Clayman D A, Faillace W J, McKee S W, Gama C H
Department of Radiology, University of Florida Health Science Center/Jacksonville 32209, USA.
AJNR Am J Neuroradiol. 1997 Apr;18(4):751-7.
We describe the clinical and radiologic changes related to progressive facial hemiatrophy (Parry-Romberg syndrome) occurring during a 20-month period in a child who presented with unilateral neurologic deficits and facial hemiatrophy. CT and MR findings included unilateral focal infarctions in the corpus callosum, diffuse deep and subcortical white matter signal changes, mild cortical thickening, and leptomeningeal enhancement with dense mineral deposition. Angiographic findings were normal. We hypothesize that a noninfectious, unilateral inflammatory process, possibly associated with a chronic vasomotor disturbance and sympathetic nerve chain inflammation, was a major factor in the pathogenesis of this syndrome.
我们描述了一名出现单侧神经功能缺损和面部半侧萎缩的儿童在20个月内发生的与进行性面部半侧萎缩（帕里-罗姆伯格综合征）相关的临床和放射学变化。CT和MR表现包括胼胝体单侧局灶性梗死、弥漫性深部和皮质下白质信号改变、轻度皮质增厚以及软脑膜强化伴致密矿物质沉积。血管造影结果正常。我们推测，一种非感染性的单侧炎症过程，可能与慢性血管运动障碍和交感神经链炎症有关，是该综合征发病机制中的一个主要因素。
