Benito Bartolomé F, Sánchez Fernández-Bernal C, Jiménez Casso S
Unidad de Arritmias, Hospital Infantil La Paz, Madrid.
Rev Esp Cardiol. 1997 Mar;50(3):205-7. doi: 10.1016/s0300-8932(97)73205-6.
Incessant ventricular tachycardia in children 2 years old or younger is usually caused by a well-localized myocardial lesion that has been termed myocardial hamartoma. Its major clinical manifestation is a rapid and potentially fatal tachyarrhythmia that does not respond to antiarrhythmic drugs. We report a patient who underwent successful surgical excision of the hamartoma and we describe the clinical features, pathologic findings and longterm follow-up.
2岁及以下儿童的持续性室性心动过速通常由一种定位明确的心肌病变引起,这种病变被称为心肌错构瘤。其主要临床表现是一种快速且可能致命的心律失常,对抗心律失常药物无反应。我们报告了一例成功接受错构瘤手术切除的患者,并描述了其临床特征、病理结果及长期随访情况。