Myrmel T, Christensen O, Lunde P
Kirurgisk avdeling, Regionsykehuset i Tromsø.
Tidsskr Nor Laegeforen. 1997 Feb 10;117(4):519-20.
Osteogenesis imperfecta is an hereditary defect in the synthesis of collagen fibres. The disease can cause cardiac defects, such as aortic and mitral incompetence. Surgical repair of these defects is complicated by tissue friability and bleeding problems. We describe a case where an incompetent aortic valve was successfully replaced by a mechanical prosthesis.
成骨不全是一种胶原蛋白纤维合成的遗传性缺陷。该疾病可导致心脏缺陷，如主动脉瓣和二尖瓣关闭不全。这些缺陷的手术修复因组织脆弱和出血问题而变得复杂。我们描述了一例主动脉瓣关闭不全患者成功植入机械瓣膜的病例。
