Fuchs J, Maschek H, von Schweinitz D, Glüer S, Mildenberger H
Department of Pediatric Surgery, Hannover Medical School, Germany.
Eur J Pediatr Surg. 1997 Apr;7(2):112-4. doi: 10.1055/s-2008-1071067.
Lymphangiomyomatosis (LAM) is a benign tumor-like lesion of lymphatic vessels with unknown etiology. 80 cases of LAM are presently described. So far, it appears that only women in their reproductive years seem to be affected. Here, we describe the first LAM in an 11-months-old infant with a presumably local form of LAM. This leads us to consider the possibility that this tumor-like lesion may originate from a hamartomateous malformation. The diagnosis is based on pre-operative sonography and CT, as well as on histological and immunohistochemical examination of the tumor.
淋巴管平滑肌瘤病（LAM）是一种病因不明的淋巴管良性肿瘤样病变。目前描述了80例LAM病例。到目前为止，似乎只有处于生育年龄的女性会受到影响。在此，我们描述了首例11个月大婴儿患局部型LAM的病例。这使我们考虑到这种肿瘤样病变可能起源于错构瘤样畸形的可能性。诊断基于术前超声检查、CT以及肿瘤的组织学和免疫组化检查。
