Kataria R, Bhatnagar V, Gupta S D, Mitra D K
Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi.
Surg Today. 1998;28(10):1084-6. doi: 10.1007/BF02483968.
Lymphangiomas and lymphangiomyomas are benign abnormal collections of lymphatic vessels which form a cystic mass. The mediastinum is an uncommon location for these hamartomas in children, but may be life-threatening. We report herein the case of a 23-month-old boy who presented with stridor and a history of recurrent respiratory tract infections. Soon after his admission he suddenly developed respiratory failure and was found to have a multiloculated, cystic mediastinal mass which was initially thought to be a lymphangioma. The mass was extensively infiltrative, and histological examination showed prominent smooth muscle proliferation in the walls of the cysts, confirming a diagnosis of lymphangiomyoma. The terminology and relevant literature on the topic are reviewed following the presentation of this case.
淋巴管瘤和淋巴管肌瘤是淋巴管的良性异常聚集，形成囊性肿块。纵隔是儿童这些错构瘤的罕见部位，但可能危及生命。我们在此报告一例23个月大的男孩，他表现为喘鸣并伴有反复呼吸道感染史。入院后不久，他突然出现呼吸衰竭，发现有一个多房性囊性纵隔肿块，最初被认为是淋巴管瘤。该肿块具有广泛的浸润性，组织学检查显示囊肿壁有明显的平滑肌增生，确诊为淋巴管肌瘤。在介绍该病例后，对该主题的术语和相关文献进行了综述。
