Garcia J P, França T, Pedroso C, Cardoso C, Cid M O
St. Martha's Hospital-General Surgery, Histopathology Ward, Lisboa, Portugal.
HPB Surg. 1997;10(4):201-9. doi: 10.1155/1997/81239.
Nesidioblastosis is an exceedingly rare occurrence in the adult and, when it appears, it is usually part of a MEA1 syndrome. We present a case of nesidioblastosis in a young woman, with no concurrent endocrine pathology, while we discuss in detail the diagnostic and therapeutic problems posed by this condition. The selected treatment was sub-total pancreatectomy (70-80%) and the histopathologic and immunohistochemical tests of the surgical specimen showed: "Diffuse Nesidioblastosis". The histopathologic and immuno-histochemical features of the resected pancreas are analysed in detail.
成人生长抑素瘤极为罕见，一旦出现，通常是多发性内分泌腺瘤1型（MEA1）综合征的一部分。我们报告一例年轻女性生长抑素瘤病例，该患者无并发内分泌病理改变，同时详细讨论了该病症所带来的诊断和治疗问题。所选治疗方法为胰腺次全切除术（70 - 80%），手术标本的组织病理学和免疫组织化学检查显示：“弥漫性生长抑素瘤”。对切除胰腺的组织病理学和免疫组织化学特征进行了详细分析。
