[Aicardi syndrome and acquired retinal detachment].

BACKGROUND

The Aicardi syndrome is a complex of congenital anomalies consisting of agenesis of the corpus callosum, infantile spasms and pathognomonic chorioretinal lacunar lesions. An acquired detachment of the retina was reported only in one patient.

HISTORY AND SIGNS

We report about a nine-month-old girl with Aicardi syndrome. She presented the typical signs of this syndrome and an acquired detachment in both eyes.

THERAPY AND OUTCOME

We performed a translimbal vitrectomy with silicon-oil instillation on the right eye.

CONCLUSION

On the basis of histological findings reported in the literature we suggest a combined pathogenesis of the ablatio retinae in our patient with Aicardi syndrome: traction and foramina.