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成人胚胎性横纹肌肉瘤对放疗显示出显著反应:一例报告

Adult embryonal rhabdomyosarcoma showing marked response to radiotherapy: a case report.

作者信息

Takahashi T, Mitsuhashi N, Sakurai H, Saito Y, Akimoto T, Kitamoto Y, Maebayashi K, Fukusato T, Niibe H

机构信息

Department of Radiology and Radiation Oncology, Gunma University School of Medicine, Maebashi, Japan.

出版信息

Radiat Med. 1997 May-Jun;15(3):177-80.

PMID:9278375
Abstract

A case of embryonal rhabdomyosarcoma (RMS) arising from adult lower proximal extremity is described. Rhabdomyosarcoma (RMS) is most common among children, but adult embryonal RMS is rare. The patient was a 44-year-old man with a large tumor of the left extremity invading to the pelvis. The histological diagnosis was embryonal RMS. Radiation therapy was delivered a total dose of 50 Gy to the tumor. Although adult RMS, usually pleomorphic type, is considered to be radioresistant, the tumor showed marked response to radiotherapy and local control was achieved easily in this case.

摘要

本文描述了一例起源于成人下肢近端的胚胎性横纹肌肉瘤(RMS)。横纹肌肉瘤(RMS)在儿童中最为常见,但成人胚胎性RMS却很罕见。该患者为一名44岁男性,左下肢有一个巨大肿瘤,已侵犯至骨盆。组织学诊断为胚胎性RMS。对肿瘤进行了总量为50 Gy的放射治疗。尽管成人RMS通常为多形性类型,被认为对放疗有抗性,但该肿瘤对放疗显示出显著反应,在本病例中很容易实现了局部控制。

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