do Amaral B, Costa e Sousa R, Moreira C G
Serviço de Estomatologia e C. Maxilo-Facial, H.G.S.A., Porto.
Acta Med Port. 1997 May;10(5):409-15.
The major features of the nevoid basal-cell carcinoma syndrome are epidermal multiple cell carcinomas, cysts of the jaws and skeletal abnormalities, mainly in the ribs. The authors have reviewed the literature concerning multiple anomalies which are associated to this syndrome, and report a clinical case, emphasizing the advantages of early diagnosis, mainly for dermal and maxillary lesions.
痣样基底细胞癌综合征的主要特征是表皮多发性细胞癌、颌骨囊肿和骨骼异常，主要累及肋骨。作者回顾了与该综合征相关的多种异常情况的文献，并报告了一例临床病例，强调了早期诊断的优势，主要针对皮肤和上颌病变。
