Shapiro K, Shulman K
J Neurosurg. 1976 Jul;45(1):20-5. doi: 10.3171/jns.1976.45.1.0020.
The authors describe two children with anomalous intracranial venous return associated with bilateral facial nevi, macrocrania, and cephalic venous hypertension. Both children had functional absence of the jugular bulbs, forcing the intracranial venous effluent to exit through persistent emissary pathways. Both children had sustained intracranial hypertension, with one child developing symptomatic communicating hydrocephalus that responded satisfactorily to shunting. The relationship between these patients and those with Sturge-Weber syndrome is discussed. The embryologic abnormality producing the anomalous venous return is characterized. The link between venous hypertension and the development of hydrocephalus is discussed. The increased cranial compliance seen in this age group may predispose certain pediatric patients to develop hydrocephalus when stressed by venous hypertension.
作者描述了两名患有颅内静脉回流异常的儿童，伴有双侧面部痣、巨颅症和头部静脉高压。两名儿童的颈静脉球均功能缺失，迫使颅内静脉流出物通过持续的导静脉途径排出。两名儿童均患有持续性颅内高压，其中一名儿童发展为有症状的交通性脑积水，分流治疗后反应良好。本文讨论了这些患者与患有斯特奇-韦伯综合征患者之间的关系。对导致静脉回流异常的胚胎学异常进行了特征描述。讨论了静脉高压与脑积水发展之间的联系。在这个年龄组中观察到的颅骨顺应性增加可能使某些儿科患者在受到静脉高压影响时易发生脑积水。
