Gamillscheg A, Beitzke A, Dacar D, Karpf E F, Stein J I, Zobel G, Haidvogl M
Klinische Abteilung für Pädiatrische Kardiologie, Universitätsklinik für Kinder- und Jugendheilkunde, Graz, Osterreich.
Z Kardiol. 1997 Jul;86(7):549-53. doi: 10.1007/s003920050094.
An unusual case of subaortic stenosis and aortic regurgitation caused by accessory mitral valve tissue in a 10 year old boy is reported. Two-dimensional and Doppler echocardiography revealed the characteristic feature of a mobile, parachute-like mass in the left ventricular outflow tract pro-lapsing into the aortic valve during systole and, thus, producing a systolic pressure gradient of 70 mm Hg between the left ventricle and aorta and causing mild aortic regurgitation. The accessory valve tissue was completely excised via an aortotomy without injury to the normal mitral and aortic valves. Two dimensional echocardiography provides excellent morphological information about the relationship between the accessory mitral valve tissue and the mitral and aortic valves, respectively. Accurate preoperative evaluation by two-dimensional echocardiography facilitates the successful surgical management of this rare condition.
报道了一名10岁男孩因二尖瓣附属组织导致主动脉瓣下狭窄和主动脉瓣关闭不全的罕见病例。二维和多普勒超声心动图显示了左心室流出道中一个可移动的、降落伞样肿物的特征，该肿物在收缩期脱垂入主动脉瓣，从而在左心室和主动脉之间产生70 mmHg的收缩期压力阶差，并导致轻度主动脉瓣关闭不全。通过主动脉切开术完全切除附属瓣膜组织，未损伤正常的二尖瓣和主动脉瓣。二维超声心动图分别提供了关于二尖瓣附属组织与二尖瓣和主动脉瓣之间关系的出色形态学信息。通过二维超声心动图进行准确的术前评估有助于成功手术治疗这种罕见疾病。
