Arnedillo A, Cubillo J M, Puente L
Servicio de Neumología, Hospital General Universitario Gregorio Marañón, Madrid.
An Med Interna. 1997 Aug;14(8):406-8.
Pulmonary arteriovenous fistulas are a very infrequent illness. The majority of these cases are associated with hereditary haemorrhagic telangiectasia, therefore their isolated presentation is exceptional. We present a patient that was diagnosed of two arteriovenous fistulas non associated with hereditary haemorrhagic telangiectasia. His main symptom was progressive dyspnea on exertion, with cyanosis and clubbing. His evolution after surgery was satisfactory. Theirs clinical, diagnosis and therapeutic peculiarities ware discussed.
肺动静脉瘘是一种非常罕见的疾病。这些病例大多数与遗传性出血性毛细血管扩张症相关,因此孤立出现的情况极为罕见。我们报告一例被诊断为患有两个与遗传性出血性毛细血管扩张症无关的动静脉瘘的患者。他的主要症状是进行性劳力性呼吸困难,伴有发绀和杵状指。术后他的病情进展令人满意。文中讨论了其临床、诊断和治疗特点。