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Cystic fibrosis transmembrane conductance regulator. Permeant ions find the pore.

作者信息

Dawson D C, Smith S S

出版信息

J Gen Physiol. 1997 Oct;110(4):337-9. doi: 10.1085/jgp.110.4.337.

DOI:10.1085/jgp.110.4.337
PMID:9379166
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2229378/
Abstract
摘要

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本文引用的文献

1
Multi-Ion mechanism for ion permeation and block in the cystic fibrosis transmembrane conductance regulator chloride channel.囊性纤维化跨膜传导调节因子氯离子通道中离子通透和阻断的多离子机制。
J Gen Physiol. 1997 Oct;110(4):365-77. doi: 10.1085/jgp.110.4.365.
2
Permeability of wild-type and mutant cystic fibrosis transmembrane conductance regulator chloride channels to polyatomic anions.野生型和突变型囊性纤维化跨膜传导调节因子氯通道对多原子阴离子的通透性。
J Gen Physiol. 1997 Oct;110(4):355-64. doi: 10.1085/jgp.110.4.355.
3
Halide permeation in wild-type and mutant cystic fibrosis transmembrane conductance regulator chloride channels.野生型和突变型囊性纤维化跨膜传导调节因子氯通道中的卤化物渗透
J Gen Physiol. 1997 Oct;110(4):341-54. doi: 10.1085/jgp.110.4.341.
4
Disulphonic stilbene block of cystic fibrosis transmembrane conductance regulator Cl- channels expressed in a mammalian cell line and its regulation by a critical pore residue.二磺酸芪对在一种哺乳动物细胞系中表达的囊性纤维化跨膜传导调节因子氯离子通道的阻断作用及其受关键孔道残基的调节
J Physiol. 1996 Nov 1;496 ( Pt 3)(Pt 3):687-93. doi: 10.1113/jphysiol.1996.sp021719.
5
Novel missense mutation (G314R) in a cystic fibrosis patient with hepatic failure.
Hum Mutat. 1996;7(2):151-4. doi: 10.1002/(SICI)1098-1004(1996)7:2<151::AID-HUMU10>3.0.CO;2-1.
6
Phosphorylation-dependent block of cystic fibrosis transmembrane conductance regulator chloride channel by exogenous R domain protein.外源性R结构域蛋白对囊性纤维化跨膜传导调节因子氯离子通道的磷酸化依赖性阻断
J Biol Chem. 1996 Mar 29;271(13):7351-6. doi: 10.1074/jbc.271.13.7351.
7
Voltage-dependent block of the cystic fibrosis transmembrane conductance regulator Cl- channel by two closely related arylaminobenzoates.两种密切相关的芳基氨基苯甲酸酯对囊性纤维化跨膜传导调节因子氯离子通道的电压依赖性阻断作用。
J Gen Physiol. 1993 Jul;102(1):1-23. doi: 10.1085/jgp.102.1.1.
8
Multi-ion pore behaviour in the CFTR chloride channel.囊性纤维化跨膜传导调节因子氯通道中的多离子孔行为
Nature. 1993 Nov 4;366(6450):79-82. doi: 10.1038/366079a0.
9
Mutations in CFTR associated with mild-disease-form Cl- channels with altered pore properties.与具有改变的孔道特性的轻度疾病形式氯离子通道相关的囊性纤维化跨膜传导调节因子（CFTR）突变。
Nature. 1993 Mar 11;362(6416):160-4. doi: 10.1038/362160a0.
10
Alternate translation initiation codons can create functional forms of cystic fibrosis transmembrane conductance regulator.交替的翻译起始密码子可产生囊性纤维化跨膜传导调节因子的功能形式。
J Biol Chem. 1995 May 19;270(20):11941-6. doi: 10.1074/jbc.270.20.11941.