Blank E, Campbell J R
Pediatrics. 1976 May;57(5):807-10.
The infant born with a posterolateral defect in the right side of the diaphragm may appear normal at birth. His abdominal viscera may be normally located; the right side of the diaphragm may seem to be intact. Later, part of the liver may herniate. As it does, it displaces the lower part of the right lung, and hepatic flexure follows into a high posterior position in the right upper quadrant of the abdomen. Rarely, obstruction of portal and hepatic venous flow at the hernial ring may cause liquid to accumulate in the right side of the chest. At any time the liver may resume its interrupted passage. Increase in herniation will quickly make the patient sicker.
出生时右侧膈肌后外侧有缺损的婴儿出生时可能看起来正常。其腹腔脏器位置可能正常;右侧膈肌似乎完整。之后,部分肝脏可能会发生疝出。随着肝脏疝出,它会推移右肺下部,肝曲随之进入右上腹的高位后方位置。极少情况下,疝环处门静脉和肝静脉血流受阻可能导致液体在右侧胸腔积聚。肝脏在任何时候都可能恢复其中断的通道。疝出增加会迅速使患者病情加重。