Graham K, Sondheimer H, Schaffer M
Department of Pediatrics, University of Colorado School of Medicine, Denver, USA.
J Heart Lung Transplant. 1997 Dec;16(12):1271-4.
A child with heterotaxia, azygous continuation of an interrupted inferior vena cava, single ventricle, and pulmonary atresia underwent the Kawashima modification of the Fontan procedure, which excluded hepatic venous return from the pulmonary blood flow. After the operation, the patient had development of pulmonary arteriovenous malformations, increasing cyanosis, and ventricular dysfunction. He underwent orthotopic heart transplantation at 7 years of age with prompt resolution of the pulmonary arteriovenous malformations.
一名患有内脏异位、中断的下腔静脉奇静脉延续、单心室和肺动脉闭锁的儿童接受了改良的川岛Fontan手术，该手术将肝静脉回流排除在肺血流之外。术后，患者出现了肺动静脉畸形、青紫加重和心室功能障碍。他在7岁时接受了原位心脏移植，肺动静脉畸形迅速得到缓解。
