Kalache K D, Chaoui R, Paris S, Bollmann R
Department of Gynecology and Obstetrics, Humboldt University, Charité School of Medicine, Berlin, Germany.
Fetal Diagn Ther. 1997 Nov-Dec;12(6):360-2. doi: 10.1159/000264506.
Unilateral lung agenesis should be suspected in fetuses presenting mediastinal shifting and absence of evidence of diaphragmatic hernia. Confirmation of diagnosis is not possible until birth as other more common lung anomalies may have a similar appearance. We present a case with right lung agenesis diagnosed at 34 weeks of gestation. Important for precise diagnosis was the color Doppler procedure, which revealed the absence of right pulmonary vessels. This is the first case in which unilateral lung agenesis has been recognized prenatally by nonvisualization of the corresponding lung vessels. The prenatally performed magnetic resonance sonography did not offer any advantages over sonography. Postnatally, the diagnosis was confirmed, and sinus venosus defect was also found. To prevent recurrent cardiopulmonary crisis, which could be caused by mediastinal shift, a tissue expander was implanted successfully at 3 months of age.
对于出现纵隔移位且无膈疝证据的胎儿，应怀疑为单侧肺发育不全。在出生前无法确诊，因为其他更常见的肺部异常可能有类似表现。我们报告一例在妊娠34周时诊断为右肺发育不全的病例。彩色多普勒检查对精确诊断很重要，其显示右肺血管缺如。这是首例通过未发现相应肺血管而在产前确诊单侧肺发育不全的病例。产前进行的磁共振超声检查相比超声检查并无优势。出生后确诊，并发现了静脉窦缺损。为预防可能由纵隔移位引起的反复心肺危机，在患儿3个月大时成功植入了组织扩张器。
