Kiefer T, Wertzel H, Freudenberg N, Hasse J
Department of Thoracic Surgery, University of Freiburg, Germany.
Thorac Cardiovasc Surg. 1997 Dec;45(6):307-9. doi: 10.1055/s-2007-1013754.
Malignant hemangiopericytoma represent less than 1% of all vascular and about 5% of all sarcomatous tumors. We are reporting the uncommon clinical case of primary pulmonary localization, of which approximately 100 cases have been published in the literature. A 54-year-old male underwent left upper lobectomy seven years ago for a tumor which proved to be a malignant hemangiopericytoma. Six months later a metastasis in the abdominal wall in the epigastrium appeared and was completely excised without further treatment. During a follow-up of 16 months another metastasis developed in the mesenterium causing ileus and leading to laparotomy with resection of 120 cm small bowel. After this procedure followed by two cycles of chemotherapy the patient remained free of disease. Details of the clinical course and a review of the literature are presented.
恶性血管外皮细胞瘤占所有血管性肿瘤的比例不到1%，占所有肉瘤性肿瘤的约5%。我们报告了一例罕见的原发性肺定位临床病例，文献中已发表了约100例此类病例。一名54岁男性七年前因肿瘤接受了左上叶切除术，术后病理证实为恶性血管外皮细胞瘤。六个月后，上腹部腹壁出现转移灶，未进行进一步治疗，该转移灶被完全切除。在16个月的随访期间，肠系膜出现了另一个转移灶，导致肠梗阻，随后进行了剖腹手术，切除了120厘米的小肠。在该手术后进行了两个周期的化疗，患者此后未再出现疾病。本文介绍了该临床病例的详细过程并对文献进行了综述。
