Hall J, Johnston K A, McPhillips J P, Barnes S D, Elston D M
Baylor College of Medicine, Texas, USA.
J Am Acad Dermatol. 1998 Feb;38(2 Pt 2):363-5. doi: 10.1016/s0190-9622(98)70585-7.
Nevoid basal cell carcinoma syndrome (NBCCS) is rare in black persons. We describe an 11-year-old black boy with NBCCS who presented with exotropia and a painful, expanding, cystic mass in the left posterior alveolar ridge. Further examination revealed odontogenic keratocysts with palmar and plantar pitting. Less than 5% of reported patients with NBCCS are black. To our knowledge, this is the first report of a black patient with NBCCS presenting with exotropia and an impacted molar displaced into the orbit by an odontogenic keratocyst.
痣样基底细胞癌综合征（NBCCS）在黑人中较为罕见。我们描述了一名患有NBCCS的11岁黑人男孩，他表现为外斜视，左后牙槽嵴有一个疼痛、不断扩大的囊性肿物。进一步检查发现有牙源性角化囊肿以及掌跖点状凹陷。报道的NBCCS患者中黑人不到5%。据我们所知，这是首例关于患有NBCCS的黑人患者出现外斜视以及一颗阻生磨牙被牙源性角化囊肿挤入眼眶的报告。
