Crenier L, Piagnerelli M, Doutrelepont J M, De Pauw L, Kinnaert P, Vereerstraeten P, Abramowicz D
Service de médecine interne, Université Libre de Bruxelles-Hôpital Erasme, Belgium.
Acta Clin Belg. 1997;52(6):401-4. doi: 10.1080/17843286.1997.11718607.
Idiopathic Systemic Capillary Leak Syndrome (SCLS) is a rare entity characterised by idiopathic increasing of capillary permeability associated with recurrent attacks of hypovolaemic shock. We report the case of a 39-year-old man with a SCLS fourteen years after a cadaveric renal transplantation. The clinical evolution was rapidly fatal despite treatment with corticoids, aminophylline and terbutaline which are the most efficient drugs known to prevent attacks.
特发性系统性毛细血管渗漏综合征（SCLS）是一种罕见的病症，其特征为特发性毛细血管通透性增加，并伴有反复发生的低血容量性休克发作。我们报告一例39岁男性患者，在尸体肾移植14年后发生了SCLS。尽管使用了皮质类固醇、氨茶碱和特布他林进行治疗（这些是已知预防发作最有效的药物），但临床病情仍迅速恶化至死亡。
