Cadman E C, Lundberg W B, Mitchell M S
Arch Intern Med. 1976 Aug;136(8):944-7.
Behçet syndrome in association with pulmonary abnormalities is rare. We described a patient with Behçet syndrome who had pulmonary involvement. A review of the literature disclosed 12 similar cases. Thrombophlebitis, superior vena cava obstruction, and hemoptysis are characteristic clinical features of patients with Behçet syndrome and pulmonary infiltrates. Once diffuse pulmonary infiltration and massive hemoptysis appear, the prognosis is poor; death from pulmonary exsanguination is likely to occur. Treatment with cyclophosphamide and prednisone, in addition to blood transfusions, may be beneficial.
白塞综合征合并肺部异常较为罕见。我们描述了一名患有肺部受累的白塞综合征患者。文献回顾发现了12例类似病例。血栓性静脉炎、上腔静脉阻塞和咯血是白塞综合征合并肺部浸润患者的典型临床特征。一旦出现弥漫性肺部浸润和大量咯血，预后较差；可能会因肺出血死亡。除输血外，使用环磷酰胺和泼尼松治疗可能有益。
