白塞病合并与支气管血管瘘相关的大量咯血：一例病例报告。

Behçet's disease presenting with massive hemoptysis related to bronchovascular fistula: A case report.

作者信息

Bedirhan Mehmet Ali, Arda Naciye, Tanrıverdi Elif, Yaran Volkan, Sansar Deniz, Cansever Levent

机构信息

Department of Thoracic Surgery, Yedikule Chest and Diseases and Thoracic Surgery Training and Research Hospital, Istanbul, Turkey.

Department of Pathology, Yedikule Chest and Diseases and Thoracic Surgery Training and Research Hospital, Istanbul, Turkey.

出版信息

Turk Gogus Kalp Damar Cerrahisi Derg. 2021 Jul 26;29(3):408-411. doi: 10.5606/tgkdc.dergisi.2021.19487. eCollection 2021 Jul.

DOI:10.5606/tgkdc.dergisi.2021.19487

PMID:34589263

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8462114/

Abstract

A 37-year-old male patient was admitted to our hospital with recurrent hemoptysis, 50 mL per day. Thoracic computed tomography showed no pathology responsible for hemoptysis. Bronchoscopy revealed mucosal infiltrations and 2 to 3-mm blotch in the lateral wall of the right lower lobe. After punch biopsy of the suspected area, massive bleeding occurred. Right lower bilobectomy was performed urgently. A bronchovascular fistula was noticed at the specimen. Pathological examination result was compatible with clinically suspected Behçet"s disease. The patient was given high-dose steroid and cyclophosphamide treatment and received azathioprine maintenance treatment for 18 months. He has been symptom-free for three-year follow-up.

摘要

一名37岁男性患者因反复咯血入院，每日咯血量为50毫升。胸部计算机断层扫描未发现导致咯血的病变。支气管镜检查发现黏膜浸润，右下叶侧壁有2至3毫米的斑点。对可疑区域进行穿刺活检后，发生了大量出血。紧急进行了右下双叶切除术。在标本中发现了支气管血管瘘。病理检查结果与临床疑似的白塞病相符。该患者接受了大剂量类固醇和环磷酰胺治疗，并接受硫唑嘌呤维持治疗18个月。经过三年随访，他一直无症状。