Yoshioka K, Sato T, Ishii T, Tanaka S, Kioka K, Harihara S, Imamoto S, Haze K, Inoue T, Fujii S
Department of Internal Medicine, Osaka City General Hospital, Miyakojima, Osaka.
Intern Med. 1998 Jan;37(1):51-5. doi: 10.2169/internalmedicine.37.51.
A rare case of peliosis hepatis associated with idiopathic restrictive cardiomyopathy is reported. A 75-year-old man was admitted for evaluation of marked edema and jaundice. Serum total bilirubin was elevated above 20 mg/dl. The liver biopsy under laparoscopy revealed marked sinusoidal dilatation and retention of red blood cells, which was consistent with a diagnosis of peliosis hepatis. Cardiac catheterization revealed right ventricular filling disturbance without specific findings on endomyocardial biopsy, suggesting idiopathic restrictive cardiomyopathy. The level of serum total bilirubin decreased in association with improvement of edema after drip infusion of furosemide therapy.
报告了一例与特发性限制性心肌病相关的肝紫癜罕见病例。一名75岁男性因明显水肿和黄疸入院评估。血清总胆红素升高至20mg/dl以上。腹腔镜下肝活检显示明显的血窦扩张和红细胞潴留，这与肝紫癜的诊断一致。心脏导管检查显示右心室充盈障碍，心内膜活检无特异性发现，提示特发性限制性心肌病。静脉滴注呋塞米治疗后，随着水肿改善，血清总胆红素水平下降。
