Goldberg B A, Erwin W D, Heggeness M H
Shriners Hospitals for Crippled Children, Houston, Texas, USA.
Spine (Phila Pa 1976). 1998 Feb 15;23(4):504-7. doi: 10.1097/00007632-199802150-00021.
A report of a case of lumbar spine duplication with the clinical appearance of adolescent scoliosis.
To increase knowledge about the pathogenesis and treatment of lumbar spinal duplication.
Although there have been other reports of lumbar spine duplication of this magnitude, these malformations typically are associated with severe neurologic abnormalities (dicephalus, myelomeningocele) or gastrointestinal abnormalities (omphalocele, neurenteric fistulas). Several investigators have recommended early surgical intervention for this abnormality because of the perceived risk of progressive neurologic abnormality from tethering of the cord.
In a 13-year-old girl who had truncal asymmetry, lumbar spine duplication was noted on plain radiographs. A magnetic resonance study was obtained, and the patient was observed with conservative treatment for 3 years.
Although extensive abnormalities were noted on the magnetic resonance images, which were related to duplication of spinal cord and vertebral bodies, the patient was neurologically intact and remained so until skeletal maturity.
This rare malformation typically has severe neurologic sequelae. Conservative management in the reported patient did not result in a progressive neurologic lesion at the time of skeletal maturity.
一例具有青少年脊柱侧凸临床表现的腰椎重复畸形病例报告。
增加对腰椎重复畸形发病机制及治疗的认识。
尽管此前已有其他关于如此严重程度腰椎重复畸形的报道,但这些畸形通常与严重的神经异常(双头畸形、脊髓脊膜膨出)或胃肠道异常(脐膨出、神经管肠瘘)相关。由于认为存在脊髓拴系导致神经功能异常进行性加重的风险,一些研究者建议对这种异常尽早进行手术干预。
在一名有躯干不对称的13岁女孩中,X线平片发现腰椎重复畸形。进行了磁共振检查,并对患者进行了3年的保守治疗观察。
尽管磁共振图像显示存在广泛异常,与脊髓和椎体重复有关,但患者神经功能正常,直至骨骼成熟时仍保持如此。
这种罕见畸形通常会导致严重的神经后遗症。报告病例中的保守治疗在骨骼成熟时未导致神经病变进展。