Ahmed S, Xenos C, Hockley A D
Department of Paediatric Neurosurgery, Birmingham Children's Hospital, UK.
Childs Nerv Syst. 2000 Sep;16(9):603-6. doi: 10.1007/PL00007301.
We present a case of an asymptomatic and neurologically normal 6-year-old girl who was noted to have a gross spinal abnormality.
Neuroimaging demonstrates gross thoraco-lumbar spine duplication, which is at the severe end of the split cord malformation (SCM) group of congenital abnormalities. Despite the position of the neural structures, the clinical condition has so far not suggested that any surgical intervention is indicated, though the girl's later growth spurts may still unmask features of a tethered spinal cord.
We present a brief review of the literature dealing with theories of embryogenesis relating to SCM, the common clinical and radiological features, and finally the surgical options available.
我们报告一例6岁无症状且神经系统正常的女孩,其被发现有明显的脊柱异常。
神经影像学显示胸腰段脊柱严重重复畸形,这属于先天性异常中的脊髓纵裂畸形(SCM)组的严重类型。尽管神经结构的位置如此,但目前临床情况并未提示需要进行任何手术干预,不过女孩日后的生长突增仍可能会显现出脊髓栓系的特征。
我们简要回顾了有关SCM胚胎发生理论、常见临床和放射学特征以及最终可用手术选择的文献。