Rubio Briones J, Regalado Pareja R, Sánchez Martín F, Chéchile Toniolo G, Huguet Pérez J, Villavicencio Mavrich H
IUNA-Fundación Puigvert, Urology Service, Barcelona, Spain.
Eur Urol. 1998;33(2):175-9. doi: 10.1159/000019551.
To know the incidence of tumoural pathology among our cases of horseshoe kidney (HK), a congenital anomaly occurring in 0.25% of the population, as well as their prognostic factors and follow-up.
A total of 82 patients admitted at our Centre between 1967 and 1996 with an HK diagnosis were retrospectively reviewed. We have collected a total of 10 cases of HK tumours. We analyse the clinical, diagnostic, surgical and evolutionary peculiarities of the different HK tumour aetiologies, as compared with those described in literature.
Our experience is based on 10 patients-5 adenocarcinomas, 4 transitional cell carcinomas and a Wilms' tumour.
We have observed that in the case of transitional cell carcinomas, the diagnosis is generally made at an advanced stage. The prognosis of the tumorous disease depends upon the same prognostic factors as in the case of normal kidneys. Renal adenocarcinoma is the kind of tumour most frequently associated with HKs. Its incidence among the HK cases is not greater than among the normal population. Conservative local treatment criteria for adenocarcinoma should be valid for HKs as well.
了解马蹄肾（HK）病例中肿瘤性病变的发生率，马蹄肾是一种先天性异常，在人群中的发生率为0.25%，并了解其预后因素及随访情况。
回顾性分析1967年至1996年期间在本中心确诊为马蹄肾的82例患者。共收集到10例马蹄肾肿瘤病例。我们分析了不同马蹄肾肿瘤病因的临床、诊断、手术及演变特点，并与文献报道的情况进行比较。
我们的经验来自10例患者，其中5例为腺癌，4例为移行细胞癌，1例为肾母细胞瘤。
我们观察到，对于移行细胞癌，通常在疾病晚期才得以诊断。肿瘤性疾病的预后取决于与正常肾脏相同的预后因素。肾腺癌是最常与马蹄肾相关的肿瘤类型。其在马蹄肾病例中的发生率并不高于正常人群。腺癌的保守局部治疗标准对马蹄肾同样适用。
