Fowler C L
Department of Surgery, University of Kentucky Medical Center, Lexington 40536-0084, USA.
J Pediatr Surg. 1998 Mar;33(3):522-4. doi: 10.1016/s0022-3468(98)90104-x.
An infant was born with a spectrum of anomalies representing a unique variant of the split notochord syndrome. The major anomalies included giant omphalocele and duplicated lower spine, between which developed a posterior lumbosacral mass that was contiguous with an intraabdominal, skin-covered "leg" within a saccular cecum. Features of this case overlap aspects of fetiform teratoma, fetus-in-fetu, conjoined twins, and caudal duplication, suggesting an etiologic relation between these entities and split notochord syndrome.
