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先天性十二指肠狭窄合并内脏反位:罕见关联。

Abdominal situs inversus with congenital duodenal stenosis: rare association.

作者信息

Akel S, Halabi J, Shawis R

机构信息

American University of Beirut Medical Center, Lebanon.

出版信息

Eur J Pediatr Surg. 1998 Feb;8(1):55-7. doi: 10.1055/s-2008-1071120.

DOI:10.1055/s-2008-1071120
PMID:9550279
Abstract

Abdominal situs inversus carries a significant mortality because the majority of cases (95 %) have associated cardiac and splenic defects. A review of all cases reported in the English literature confirms in addition the presence of significant gastro-intestinal pathologies, mainly annular pancreas, midgut volvulus and duodenal atresia. We report on an additional case of abdominal situs inversus without cardiac or splenic abnormalities, who had partial duodenal obstruction secondary to a mucosal diaphragm. This seems to be the thirteenth case associated with duodenal obstruction and the sixth case secondary to a mucosal duodenal diaphragm, to date, in this setting.

摘要

内脏反位具有较高的死亡率,因为大多数病例(95%)伴有心脏和脾脏缺陷。对英文文献中报道的所有病例进行回顾还证实,存在明显的胃肠道病变,主要是环状胰腺、中肠扭转和十二指肠闭锁。我们报告了一例额外的内脏反位病例,该病例无心脏或脾脏异常,因黏膜隔膜导致十二指肠部分梗阻。这似乎是迄今为止在这种情况下与十二指肠梗阻相关的第13例病例,也是继发于十二指肠黏膜隔膜的第6例病例。

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引用本文的文献

1
Congenital Duodenal Obstruction, Situs Inversus Totalis, and Gastric Perforation in a Neonate.一名新生儿的先天性十二指肠梗阻、完全性内脏反位和胃穿孔
J Neonatal Surg. 2017 Apr 15;6(2):35. doi: 10.21699/jns.v5i4.463. eCollection 2017 Apr-Jun.
2
Duodenal atresia in association with situs inversus abdominus.十二指肠闭锁合并腹内脏器反位。
J Indian Assoc Pediatr Surg. 2012 Apr;17(2):71-2. doi: 10.4103/0971-9261.93967.
3
Congenital duodenal obstruction with situs inversus totalis: Report of a rare association and discussion.
先天性十二指肠梗阻合并完全性内脏转位:罕见关联病例报告及讨论
J Indian Assoc Pediatr Surg. 2008 Apr;13(2):77-8. doi: 10.4103/0971-9261.43029.
4
Prenatal diagnosis of annular pancreas: reliability of the double bubble sign with periduodenal hyperechogenic band.环状胰腺的产前诊断:十二指肠周围高回声带双泡征的可靠性
Fetal Diagn Ther. 2008;24(4):483-90. doi: 10.1159/000178759. Epub 2008 Dec 1.
5
Congenital intrinsic duodenal obstruction: a review of 35 cases.先天性十二指肠内梗阻:35例病例回顾
Ann Saudi Med. 2007 Jul-Aug;27(4):289-92. doi: 10.5144/0256-4947.2007.289.
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Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature.腹内脏器反位合并先天性十二指肠梗阻:两例报告及文献复习
Pediatr Surg Int. 2005 Jul;21(7):589-92. doi: 10.1007/s00383-005-1412-y. Epub 2005 Jul 13.
7
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Pediatr Surg Int. 2004 Apr;20(4):301-3. doi: 10.1007/s00383-003-1132-0. Epub 2004 May 20.