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十二指肠闭锁合并腹内脏器反位。

Duodenal atresia in association with situs inversus abdominus.

作者信息

Shankar Raghu, Rao Sadashiva P, Shetty Kishan B

机构信息

Department of Surgery, Pediatric Surgery Unit, Kasturba Medical College, Manipal University, Mangalore, Karnataka, India.

出版信息

J Indian Assoc Pediatr Surg. 2012 Apr;17(2):71-2. doi: 10.4103/0971-9261.93967.

DOI:10.4103/0971-9261.93967
PMID:22529552
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3326826/
Abstract

We report a rare association of duodenal atresia with situs inversus abdominus in a newborn. The infantogram revealed "reverse double-bubble sign" without dextrocardia. The sonography and echocardiography confirmed the diagnosis of situs inversus abdominus with multiple cardiac anomalies. Laparotomy and a duodenoduodenostomy were carried out.

摘要

我们报告了一例新生儿十二指肠闭锁合并腹内脏器反位的罕见病例。婴儿X线照片显示“反向双泡征”,无右位心。超声检查和超声心动图证实了腹内脏器反位并伴有多种心脏异常的诊断。实施了剖腹手术和十二指肠十二指肠吻合术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90bf/3326826/3bac99006e77/JIAPS-17-71-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90bf/3326826/3bac99006e77/JIAPS-17-71-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90bf/3326826/3bac99006e77/JIAPS-17-71-g001.jpg

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Preduodenal Portal Vein with Situs Inversus Totalis causing Duodenal Obstruction.十二指肠前门静脉合并完全性内脏反位导致十二指肠梗阻。

本文引用的文献

1
Congenital duodenal obstruction with situs inversus totalis: Report of a rare association and discussion.先天性十二指肠梗阻合并完全性内脏转位:罕见关联病例报告及讨论
J Indian Assoc Pediatr Surg. 2008 Apr;13(2):77-8. doi: 10.4103/0971-9261.43029.
2
Situs anomalies and gastrointestinal abnormalities.脏器位置异常与胃肠道异常。
J Pediatr Surg. 2006 Jul;41(7):1237-42. doi: 10.1016/j.jpedsurg.2006.03.045.
3
Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature.
APSP J Case Rep. 2016 Jun 15;7(3):24. doi: 10.21699/ajcr.v7i3.435. eCollection 2016 Jul-Aug.
腹内脏器反位合并先天性十二指肠梗阻:两例报告及文献复习
Pediatr Surg Int. 2005 Jul;21(7):589-92. doi: 10.1007/s00383-005-1412-y. Epub 2005 Jul 13.
4
Genetics of human situs abnormalities.人类内脏位置异常的遗传学
Am J Med Genet. 2001 Jul 15;101(4):356-8.
5
Abdominal situs inversus with congenital duodenal stenosis: rare association.先天性十二指肠狭窄合并内脏反位:罕见关联。
Eur J Pediatr Surg. 1998 Feb;8(1):55-7. doi: 10.1055/s-2008-1071120.