Hayashi R, Tachikawa H, Watanabe R, Honda M, Katsumata Y
Department of Neurology, Yokohama City Hospital, Kanagawa.
Intern Med. 1998 Feb;37(2):166-8. doi: 10.2169/internalmedicine.37.166.
Familial hemiplegic migraine (FHM) is an autosomal dominant syndrome characterized by recurrent episodes of varying degrees of hemiparesis associated with migraine. The aura including hemiparesis may be prolonged and in severe attacks may often be associated with confusion or coma. We describe a case of FHM whose aura was atypically prolonged and resulted in irreversible brain deficit which on magnetic resonance imaging (MRI) was suggestive of cortical hyperperfusion. A subsequent MRI showed left brain atrophy.
家族性偏瘫性偏头痛（FHM）是一种常染色体显性综合征，其特征为与偏头痛相关的不同程度偏瘫反复发作。包括偏瘫在内的先兆可能会延长，在严重发作时常常伴有意识模糊或昏迷。我们描述了一例FHM病例，其先兆非典型延长并导致不可逆的脑功能缺损，磁共振成像（MRI）显示为皮质血流灌注过多。随后的MRI显示左侧脑萎缩。
