Sanni R B, Coulibaly-Denoulet D, Coulibaly B, Nandiolo R, Mobiot M L
Service de Chirurgie Pédiatrique, CHU de Treichville, Abidjan, Côte-d'Ivoire.
Ann Urol (Paris). 1998;32(1):23-7.
Over the past 10 years, we have seen sixteen children (15 males and 1 female) with the prune-belly syndrome. We have managed 12 of these children, but 4 of them were never reviewed. Abdominal wall reconstruction was performed in 11 children by dissection of spermatic vessels and fixing the testis in the scrotum. Because of our conservative approach to the management of urinary tract dilatation, we performed only one nephrostomy and 3 unilateral nephro-ureterectomies. Seven children were reviewed. The result of abdominal wall reconstruction was good in terms of cosmetic appearance and psychologic effect for the parents; we have observed no atrophic testes after orchidopexy. One of these children suffers from chronic renal failure, while the other children have good renal function. Prune-belly syndrome is a disease with a broad spectrum. The prognosis depends on the degree of renal dysplasia. These children require long-term follow-up.
在过去10年里，我们诊治了16例患有梅干腹综合征的儿童（15名男性，1名女性）。我们对其中12名儿童进行了治疗，但有4名儿童从未接受复查。11名儿童通过精索血管解剖及将睾丸固定于阴囊进行了腹壁重建。由于我们对尿路扩张采取保守治疗方法，仅进行了1例肾造瘘术和3例单侧肾输尿管切除术。7名儿童接受了复查。腹壁重建在外观和对家长的心理影响方面效果良好；我们观察到睾丸固定术后没有睾丸萎缩的情况。其中1名儿童患有慢性肾衰竭，而其他儿童肾功能良好。梅干腹综合征是一种具有广泛谱系的疾病。预后取决于肾发育异常的程度。这些儿童需要长期随访。
