Pilz P, Hartjes H J
Stroke. 1976 Jul-Aug;7(4):393-8. doi: 10.1161/01.str.7.4.393.
A 16-year-old boy, who had sudden left-sided hemiplegia, died two weeks following onset of symptoms. A right carotid angiogram showed stenosis at the termination of the internal carotid artery. The middle cerebral artery had a beaded appearance and some of its branches were occluded. A basal "moyamoya" syndrome and transdural anastomoses were present. At autopsy, multiple intracranial dissecting aneurysms were found. Arteries of the body displayed fibromuscular dysplasia (FMD). The relevance of dysplastic changes of intracranial arteries and the relationship to moyamoya syndrome are discussed.
一名16岁男孩突发左侧偏瘫，症状出现两周后死亡。右侧颈动脉血管造影显示颈内动脉末端狭窄。大脑中动脉呈串珠样外观，其一些分支闭塞。存在基底节区“烟雾病”综合征及经硬膜吻合。尸检发现多个颅内夹层动脉瘤。身体其他部位的动脉显示纤维肌发育不良（FMD）。本文讨论了颅内动脉发育异常的相关性及其与烟雾病综合征的关系。
