Fridge J L, Vichinsky E P
Department of Hematology/Oncology, Children's Hospital Oakland, California 94609, USA.
J Pediatr. 1998 May;132(5):871-3. doi: 10.1016/s0022-3476(98)70321-x.
Severe forms of epidermolysis bullosa result in a transfusion-dependent chronic anemia and are fatal. The cause of the anemia is unknown. We evaluated five children whose anemia failed to respond to oral iron but who became transfusion independent after treatment with intravenous iron and human recombinant erythropoietin.
严重型大疱性表皮松解症会导致依赖输血的慢性贫血，且会致命。贫血的病因尚不清楚。我们评估了五名儿童，他们的贫血对口服铁剂无反应，但在接受静脉注射铁剂和重组人促红细胞生成素治疗后不再依赖输血。
