Sarihan H, Abes M, Yildiz K, Turgutalp H, Arslan Y
Department of Pediatric Surgery, Karadeniz Technical University, Faculty of Medicine, Trabzon, Turkey.
Eur J Pediatr Surg. 1998 Apr;8(2):107-10. doi: 10.1055/s-2008-1071134.
Two rare cases of mesenteric fibromatosis are presented. The first patient had a right upper quadrant mass and colicky abdominal pain. The tumor originated from the mesentery of the colon and it infiltrated the gallbladder, cystic duct, and the liver. The second patient had severe hematemesis and melena. The origin of the tumor, which infiltrated 3/4 part of the stomach, the gastrohepatic ligament, the first part of the duodenum, and the liver could not be determined. In the first patient, partial colectomy and cholecystectomy were performed and the liver lesion was completely excised. The second patient underwent subtotal gastrectomy and left lobectomy of the liver. The first part of the duodenum was excised. Gastrojejunostomy was performed. No recurrence was recorded in either patients during 16 and 13 months follow-up, respectively. In this report, diagnostic aids, differential diagnosis and treatment of this rare disease are discussed.
本文报告两例罕见的肠系膜纤维瘤病。首例患者有右上腹肿块及绞痛性腹痛。肿瘤起源于结肠系膜，侵犯了胆囊、胆囊管及肝脏。第二例患者有严重呕血及黑便。肿瘤侵犯胃的3/4、胃肝韧带、十二指肠第一部及肝脏，其起源无法确定。首例患者行部分结肠切除术及胆囊切除术，肝脏病变被完整切除。第二例患者行胃次全切除术及肝左叶切除术，十二指肠第一部被切除，并行胃空肠吻合术。分别随访16个月和13个月，两例患者均无复发。本文讨论了这种罕见疾病的诊断辅助手段、鉴别诊断及治疗。
